Abstract
Autoimmune pancreatitis (AIP) is a disease of unknown aetiology, which in part belongs into the novel group of diseases known as IgG4-related disease. Characteristic histomorphology, tissue infiltration by IgG4 positive plasma cells and elevated serum IgG4 concentration are the components of the diagnostic criteria, but in isolation they are quite non-specific findings.
This short review is aimed at diagnosis of IgG4-related AIP, with emphasis on limits and potential pitfalls in the clinical and pathological praxis.