Solitary angiokeratoma does not belong to the most frequently seen cutaneous conditions in daily praxis, however, detailedknowledge and understanding of the histological structure can be helpful in diagnostics and it can help in selections of aneffective treatment. Multiple angiokeratomas are exceedingly rare.
The knowledge of their association with other systemic disorderscan be invaluable for clinicians. By correct recognition of angiokeratomas, any dermatologist can help to shed light on yetunrecognized conditions in patients.