Abstract
Use of noninvasive technical support of brething is increasing in children with chronic diseases of different etiology. These patients are recruited mainly from those, whose underlying condition affects the respiratory muscles.
Impaired function of respiratory muscles leads to respiratory dysbalance and decreased effectiveness of the mucociliary clearance. Noninvasive ventilation and technically assisted cough can help to rebuild this respiratory balance.
The type of noninvasive ventilation depends on the pathophysiological features of the respiratory failure, indications and technical aspects should be held by skilled multidisciplinary teams with technical competence. Setting up the cough assist device and evaluation of the mucociliary clearance has to be done by skilled respiratory therapist.
The great heterogeneity of disorders, age ranges of affected children and their different prognoses present a challenge not only for the multidisciplinary team, but also for patient's family.